Table : TABLE 10.1 DIFFERENCES OF SEXUAL DEVELOPMENT
Differences of Sexual DevelopmentFrequency
Intersex (atypical genitalia)1 in 1,500 births
Klinefelter’s syndrome1 in 1,000 births
Turner’s syndrome1 in 2,500 female births
Androgen-insensitivity syndrome1 in 13,000 births
5-alpha reductase deficiencyVery rare—incidence unknown
People with ambiguous sexual characteristics are considered to have differences of sexual development. Listed above are the frequency estimates for some common causes of intersexuality.

SOURCES: GENETICS HOME REFERENCE (2008); INTERSEX SOCIETY OF NORTH AMERICA (2008); NATIONAL INSTITUTES OF HEALTH, EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT (N.D.).